CONGENITAL MALFORMATION OF THE LIVER IN A NEWBORN (CLINICAL CASE)
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Abstract
Congenital hyperplasia of the intrahepatic bile ducts refers to early fetopathy. It represents a «bizarre» proliferation of bile ducts in the portal tract with excessive development of connective tissue. A frequent complication of this defect is the attachment of secondary purulent cholangitis. When combined with small cystic kidney disease, death occurs from renal failure in the first days of life.
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